Congenital Nasal Pyriform Aperture Stenosis

Patients with congenital nasal pyriform aperture stenosis typically present with respiratory distress, including noisy breathing resembling snoring, apneic episodes during wakefulness and sleep, feeding difficulties, and failure to thrive. Sudden airway obstruction may occur but can be temporarily relieved by crying. Imaging plays a key role in diagnosis, with a pyriform aperture width of <11 mm considered diagnostic. While surgical intervention can be curative, the timing of surgery should be individualized based on symptom severity and overall prognosis. Supportive care remains essential to optimize outcomes and ensure the best possible management approach.