Double Aortic Arch Case

Double aortic arch is a congenital vascular anomaly of the primitive aortic arches that leads to compression of the trachea and/or the esophagus. Children with a double aortic arch usually present with nonspecific signs of tracheal/esophageal compression such as dysphagia, cough, respiratory failure, and choking. Consequently, vascular rings such as the double aortic arch are often found incidentally on imaging and may be further evaluated using transthoracic echocardiography, MR angiography, or CTA. Management of symptomatic cases of double aortic arch involves surgical repair in which the nondominant branch is resected, leading to an excellent prognosis and survival.